Arachnodactyly
Dolichostenomelia; Spider fingers; AchromachiaArachnodactyly is a condition in which the fingers are long, slender, and curved. They look like the legs of a spider (arachnid).
Considerations
Long, slender fingers can be normal and not associated with any medical problems. In some cases, however, "spider fingers" can be a sign of an underlying disorder.
Causes
Causes may include:
- Homocystinuria
Homocystinuria
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When to Contact a Medical Professional
Some children are born with arachnodactyly. It may become more evident over time. Talk to your health care provider if your child has long, slender fingers and you are concerned that an underlying condition may exist.
What to Expect at Your Office Visit
The provider will perform a physical exam. You will be asked questions about the medical history. This includes:
- When did you first notice the fingers being shaped like this?
- Is there any family history of early death? Is there any family history of known hereditary disorders?
- What other symptoms are present? Have you noticed any other unusual things?
Diagnostic tests are most often not necessary unless a hereditary disorder is suspected.
References
Doyle Al, Doyle JJ, Dietz HC. Marfan syndrome. In: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Textbook of Pediatrics. 21st ed. Philadelphia, PA: Elsevier; 2020:chap 722.
Grahame R, Hakim AJ. Arachnodactyly--a key to diagnosing heritable disorders of connective tissue. Nat Rev Rheumatol. 2013;9(6):358-364. PMID: 23478494 pubmed.ncbi.nlm.nih.gov/23478494/.
Herring JA. Orthopaedic-related syndromes. In: Herring JA, ed. Tachdjian's Pediatric Orthopaedics. 6th ed. Philadelphia, PA: Elsevier; 2022:chap 37.
Review Date: 12/31/2023
Reviewed By: Mary J. Terrell, MD, IBCLC, Neonatologist, Cape Fear Valley Medical Center, Fayetteville, NC. Review provided by VeriMed Healthcare Network. Also reviewed by David C. Dugdale, MD, Medical Director, Brenda Conaway, Editorial Director, and the A.D.A.M. Editorial team.